血友病（Hemophilia）是一组遗传性出血性疾病，其在凝血第一阶段凝血活 酶发生障碍。它包括血友病甲、血友病乙和血友病丙3种类型。其中血友病甲（HernophiliaA）又称凝血因子Ⅷ缺乏症或称抗血友病因子A（Antihemophilia facorA）缺乏症。真性血友病及抗血友病球蛋白缺乏症，是传统的血友病；血友病己又称凝血因子Ⅸ缺乏症或血浆凝血活酶（PIC）缺乏症；血友病丙又称凝血因子Ⅺ缺乏症、血浆凝血活酶前质（PTA）缺乏症。在先天性出血性疾病中以血友病最为常见，尤其血友病甲，约占85％，其次是血友病乙，最少见的是血友病丙。

 

 

 

Top Terms	Publications
‍ Hemophilia A		18,817
‍ Humans		17,624
‍ Patients		9,000
‍ Factor VIII		8,450
‍ Adult		5,888
‍ Hemorrhage		5,127
‍ Child		4,360
‍ Adolescent		3,798
‍ coagulation		3,609
‍ Hemophilia B		3,581
‍ Middle Aged		3,107
‍ Factor IX		2,717
‍ Antibodies		2,534
‍ antigen binding		2,448
‍ Genes		2,258
‍ Blood Coagulation Factors		2,156
‍ Viruses		2,094
‍ Child, Preschool		2,079
‍ Diagnosis		2,015
‍ Evaluation Studies as Topic		1,985
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