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进行性骨化性肌炎(MOP)又叫进行性骨化性纤维发育不良(FOP),是一种罕见的遗传性、进行性结缔组织疾患,以先天性拇指畸形和进行性横纹肌骨化为特征。国外统计其发病率约为1/200万,无性别、种族等差异,而据国内报道男性略多于女性。http://baike.baidu.com/view/3439289.htm
17岁少女患怪病恐变“活雕像” http://www.chinanews.com/gj/2013/07-30/5099339.shtml
从1907年至今,全球大概有700例,至今还没有有效的治疗方法,激素治疗、物理疗法、放射疗法、外科手术都不管用。
Fibrodysplasia Ossificans Progressiva
| | | ||||
1 2 3 ...189 | | | ||||
Top Terms |
Publications |
| ||||
---|---|---|---|---|---|---|
Myositis Ossificans |
|
1,973 | ||||
Humans |
|
1,544 | ||||
Myositis |
|
1,229 | ||||
Adult |
|
655 | ||||
Patients |
|
505 | ||||
Child |
|
474 | ||||
Tissues |
|
451 | ||||
Adolescent |
|
439 | ||||
Muscles |
|
433 | ||||
Diagnosis |
|
429 | ||||
Diagnosis, Differential |
|
417 | ||||
Ossification, Heterotopic |
|
348 | ||||
Middle Aged |
|
338 | ||||
Child, Preschool |
|
234 | ||||
Wounds and Injuries |
|
233 | ||||
Neoplasms |
|
211 | ||||
Osteogenesis |
|
198 | ||||
ossification |
|
196 | ||||
Tomography, X-Ray Computed |
|
181 | ||||
Aged |
|
161 | ||||
1 2 3 ...189 | | |
| | | ||||
1 2 3 4 5 | | | ||||
Top Years |
Publications |
| ||||
---|---|---|---|---|---|---|
2012 |
|
77 | ||||
2011 |
|
65 | ||||
2010 |
|
65 | ||||
1998 |
|
58 | ||||
2009 |
|
50 | ||||
2008 |
|
46 | ||||
2006 |
|
46 | ||||
1995 |
|
41 | ||||
2007 |
|
40 | ||||
1999 |
|
39 | ||||
1992 |
|
39 | ||||
2005 |
|
38 | ||||
1976 |
|
38 | ||||
1967 |
|
38 | ||||
1994 |
|
37 | ||||
2000 |
|
36 | ||||
2003 |
|
36 | ||||
1996 |
|
36 | ||||
1990 |
|
35 | ||||
2004 |
|
34 | ||||
1 2 3 4 5 | | |
| | | ||||
1 2 3 4 | | | ||||
Top Countries |
Publications |
| ||||
---|---|---|---|---|---|---|
United States |
|
335 | ||||
United Kingdom |
|
67 | ||||
Japan |
|
58 | ||||
France |
|
45 | ||||
India |
|
42 | ||||
Italy |
|
38 | ||||
Germany |
|
36 | ||||
Turkey |
|
34 | ||||
China |
|
27 | ||||
Belgium |
|
25 | ||||
Spain |
|
22 | ||||
Australia |
|
16 | ||||
Brazil |
|
14 | ||||
South Korea |
|
13 | ||||
Canada |
|
13 | ||||
Netherlands |
|
13 | ||||
Switzerland |
|
11 | ||||
Israel |
|
10 | ||||
Iran |
|
7 | ||||
Taiwan |
|
7 | ||||
1 2 3 4 | | |
| | | ||||
1 2 3 ...20 | | | ||||
Top Cities |
Publications |
| ||||
---|---|---|---|---|---|---|
Philadelphia |
|
95 | ||||
Paris |
|
16 | ||||
London |
|
15 | ||||
Boston |
|
14 | ||||
New York City |
|
14 | ||||
Tokyo |
|
10 | ||||
İstanbul |
|
10 | ||||
Oxford |
|
9 | ||||
New Delhi |
|
9 | ||||
Ankara |
|
8 | ||||
Madrid |
|
7 | ||||
Roma |
|
7 | ||||
Leuven |
|
7 | ||||
Beijing |
|
7 | ||||
Washington, D.C. |
|
7 | ||||
Baltimore |
|
7 | ||||
Brussels |
|
7 | ||||
İzmir |
|
6 | ||||
Saitama |
|
6 | ||||
Saint Louis |
|
6 | ||||
1 2 3 ...20 | | |
| | | ||||
1 2 3 ...40 | | | ||||
Top Journals |
Publications |
| ||||
---|---|---|---|---|---|---|
Clin Orthop Relat R |
|
69 | ||||
J Bone Joint Surg Am |
|
48 | ||||
Skeletal Radiol |
|
38 | ||||
Proc R Soc Med |
|
36 | ||||
Clin Nucl Med |
|
23 | ||||
J Bone Joint Surg Br |
|
20 | ||||
Orthopedics |
|
15 | ||||
Pediatr Radiol |
|
14 | ||||
J Bone Miner Res |
|
13 | ||||
Acta Orthop Belg |
|
13 | ||||
J Radiol |
|
13 | ||||
Am J Roentgenol |
|
13 | ||||
Am J Med Genet A |
|
12 | ||||
Radiology |
|
12 | ||||
Rofo-fortschr Rontg |
|
12 | ||||
Z Orthop Grenzgeb |
|
12 | ||||
Acta Chir Orthop Traumatol Cech |
|
11 | ||||
Indian Pediatr |
|
11 | ||||
Oral Surg Oral Med Oral Pathol |
|
11 | ||||
Clin Radiol |
|
10 | ||||
1 2 3 ...40 | | |
| | | ||||
1 2 3 ...282 | | | ||||
Top Authors |
Publications |
| ||||
---|---|---|---|---|---|---|
Kaplan F |
|
76 | ||||
Shore E |
|
49 | ||||
Zasloff M |
|
32 | ||||
Gannon F |
|
15 | ||||
Glaser D |
|
13 | ||||
Rocke D |
|
10 | ||||
Hahn G |
|
9 | ||||
Connor J |
|
9 | ||||
Billings P |
|
7 | ||||
Tabas J |
|
7 | ||||
Kransdorf M |
|
6 | ||||
Michelsson J |
|
6 | ||||
Evans D |
|
6 | ||||
Witwicki T |
|
6 | ||||
Le Merrer M |
|
5 | ||||
Lucotte G |
|
5 | ||||
Fiori J |
|
5 | ||||
McCarthy E |
|
5 | ||||
Feldman G |
|
5 | ||||
Connor J |
|
5 | ||||
1 2 3 ...282 | | |
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